Medium Sized Arteries (MSA-WG)

Clinical Practice Guidelines (CPGs) adopted

The Medium Sized Arteries Working Group (MSA-WG) follows (and have generated) existing (national and international) guidelines. The guidelines reflect the latest scientific evidence and are regularly reviewed and updated to ensure they remain up-to-date.

Results (8)
























The Ehlers-Danlos syndromes
March 03 2023

Malfait F, Castori M, Francomano CA, Giunta C, Kosho T, Byers PH. The Ehlers-Danlos syndromes. Nat Rev Dis Primers. 2020 Jul 30;6(1):64. doi: 10.1038/s41572-020-0194-9. PMID: 32732924.


Diagnosis, natural history, and management in vascular Ehlers-Danlos syndrome
March 03 2023

Diagnosis, natural history, and management in vascular Ehlers-Danlos syndrome. Byers PH, Belmont J, Black J, De Backer JFrank M, Jeunemaitre X, Johnson D, Pepin M, Robert L, Sanders L, Wheeldon N. Am J Med Genet C Semin Med Genet. 2017 Mar;175(1):40-47. doi: 10.1002/ajmg.c.31553. Review. PMID: 28306228


Abdominal emergencies in type IV ehlers-Danlos syndrome
March 03 2023

Benchellal ZA, Huten N, Danquechin Dorval E, Podeur L, Rahili A, Lemeret S, De Muret A. Abdominal emergencies in type IV ehlers-Danlos syndrome. Gastroenterol Clin Biol. 1998 Mar;22(3):343-5. French


Recommendations for anesthesia and perioperative management in patients with Ehlers-Danlos syndrome(s)
March 03 2023

Wiesmann T, Castori M, Malfait F, Wulf H. Recommendations for anesthesia and perioperative management in patients with Ehlers-Danlos syndrome(s). Orphanet J Rare Dis. 2014 Jul 23;9:109. doi: 10.1186/s13023-014-0109-5. Review


Canadian Cardiovascular Society position statement on the management of thoracic aortic disease
March 03 2023

Boodhwani M, Andelfinger G, Leipsic J, Lindsay T, McMurtry MS, Therrien J, Siu SC; Canadian Cardiovascular Society. Canadian Cardiovascular Society position statement on the management of thoracic aortic disease. Can J Cardiol. 2014 Jun;30(6):577-89.


Ehlers-Danlos syndrome: how to diagnose and when to perform genetic tests
March 03 2023

Sobey G. Ehlers-Danlos syndrome: how to diagnose and when to perform genetic tests. Arch Dis Child2015 Jan;100(1):57-61


Treatment of vascular Ehlers-Danlos syndrome: a systematic review
March 03 2023

Bergqvist D, Björck M, Wanhainen A. Treatment of vascular Ehlers-Danlos syndrome: a systematic review. Ann Surg. 2013 Aug;258(2):257-61. doi: 10.1097/SLA.0b013e31829c7a59. Review


Management of pregnancy in women with genetic disorders, Part 1: Disorders of the connective tissue, muscle, vascular, and skeletal systems
March 03 2023

Chetty SP, Shaffer BL, Norton ME. Management of pregnancy in women with genetic disorders, Part 1: Disorders of the connective tissue, muscle, vascular, and skeletal systems.Obstet Gynecol Surv. 2011 Nov;66(11):699-709. Review


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